Image of a neural disease that would cause high-frequency hearing loss.

Do you spend much time considering your nervous system? For the majority of people, the answer would probably be not very frequently. As long as your body is performing in the way that it should, you have no reason to consider how your neurons are firing or whether nerves are sending proper messages along the electrical corridors of your body. But you tend to pay more attention when something goes wrong and the nerves start to misfire.

There’s one particular condition, known as Charcot-Marie-Tooth (CMT) disease, which can influence the nervous system on a fairly large scale, though the symptoms usually manifest chiefly in the extremities. high-frequency hearing loss can also be the result of CMT according to some evidence.

What Is Charcot-Marie-Tooth Disease?

Charcot-Marie-Tooth disease is a set of inherited disorders. The protective sheathing around the nerves malfunction due to a genetic disorder.

As a result, the signals sent from your brain to those nerves (and from those nerves back to your brain) don’t progress all that well. A loss of motor function and sensation can be the outcome.

A mix of genetic factors usually leads to the manifestation of symptoms, so CMT can be present in several variations. Symptoms of CMT commonly begin in the feet and work their way up to the arms. And, high-frequency hearing loss, oddly, has a high rate of occurrence among those who have CMT.

The Cochlear Nerve: A Link Between CMT and Loss of Hearing

The connection between CMT and loss of hearing has always been colloquially recognized (that is, everyone knows somebody who has a tells about it – at least within the CMT culture). And it was hard to grasp the connection between loss of sensation in the legs and issues with the ears.

The connection was firmly established by a scientific study just recently when a group of researchers examined 79 people with CMT at the University of Iowa Hospitals and Clinics.

The results were rather conclusive. Low to moderate frequencies were heard almost perfectly by those who had CMT. But high-frequency sounds (in the moderate region in particular) were effortlessly heard by all of the participants. high-frequency hearing loss, according to this study, is likely to be linked to CMT.

What is The Cause of Hearing Loss And How Can it be Treated?

The link between high-frequency hearing loss and CMT could, at first, seem puzzling. Like all other parts of your body rely on correctly functioning nerves. Your ears are the same.

The hypothesis is, CMT impacts the cochlear nerve so sounds in the high-frequency range aren’t able to be translated. Anybody with this type of hearing loss will have a hard time hearing certain sounds, and that includes voices. Notably, make out voices in crowded or noisy rooms can be a tangible challenge.

Hearing aids are usually used to manage this type of hearing loss. There’s no known cure for CMT. Modern hearing aids can select the precise frequencies to amplify which can give considerable help in battling high-frequency hearing loss. Also, most modern hearing aids can be calibrated to work well in noisy surroundings.

There Could be Various Causes For Hearing Loss

Researchers still aren’t entirely sure why CMT and loss of hearing seem to co-exist quite so often (above and beyond their untested hypothesis). But hearing aid tech provides an obvious solution to the symptoms of that hearing loss. That’s why many individuals with CMT will make time to get a consultation with a hearing professional and get a fitting for a custom hearing aid.

There are a variety of causes for hearing loss symptoms. In some cases, hearing loss is triggered by undesirable exposure to harmful noises. Blockages can be yet another cause. It also appears that CMT is another possible cause.

The site information is for educational and informational purposes only and does not constitute medical advice. To receive personalized advice or treatment, schedule an appointment.

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